A clinical case of acquired form of thrombotic thrombocytopenic purpura. Description and treatment
Abstract
In the article have described symptoms and ongoing treatment of the acquired form of thrombotic thrombocytopenic purpura.Thrombotic thrombocytopenic purpura is a rare disease with a frequency of 4:1000000 population. It is characterized by an extremely aggressive course and high mortality in the absence of treatment (up to 90%). Often has no specific symptoms. The condition for clinical diagnosis (in the absence of other causes) is the presence of at least two symptoms: thrombocytopenia, microangiopathic hemolytic anemia.
About the Authors
D. K. Novik
ГУ «РНПЦ радиационной медицины и экологии человека»
Russian Federation
Russian Federation
A. V. Denisov
ГУ «РНПЦ радиационной медицины и экологии человека»
Russian Federation
Russian Federation
E. M. Repchenko
ГУ «РНПЦ радиационной медицины и экологии человека»
Russian Federation
Russian Federation
D. V. Kravchenko
ГУ «РНПЦ радиационной медицины и экологии человека»
Russian Federation
Russian Federation
S. G. Kuzniatsou
ГУ «РНПЦ радиационной медицины и экологии человека»
Russian Federation
Russian Federation
S. A. Khadanovich
ГУ «РНПЦ радиационной медицины и экологии человека»
Russian Federation
Russian Federation
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Review
For citations:
Novik D.K., Denisov A.V., Repchenko E.M., Kravchenko D.V., Kuzniatsou S.G., Khadanovich S.A. A clinical case of acquired form of thrombotic thrombocytopenic purpura. Description and treatment. Medical and Biological Problems of Life Activity. 2019;(2):124-128. (In Russ.)
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