medbioМедико-биологические проблемы жизнедеятельностиMedical and Biological Problems of Life Activity2074-2088Республиканский научно-практический центр радиационной медицины и экологии человека10.58708/2074-2088.2025-3(35)-63-74medbio-479Research ArticleКЛИНИЧЕСКАЯ МЕДИЦИНАCLINICAL MEDICINEРегистр первичных иммунодефицитов в Республике Беларусь: 20-летний опытRegistry of primary immunodeficiencies in the Republic of Belarus: 20-year experienceБелевцевМ. В.BelevtsevM.

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ШараповаС. О.SharapovaS.

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ГурьяноваИ. Е.GuryanovaI.

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ЖаранковаЮ. С.ZharankovaYu.

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ПоляковаЕ. А.PolyakovaE.

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АлешкевичС. Н.AleshkevichS.

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СаковичИ. С.SakovichI.

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КупчинскаяА. Н.KupchinskayaA.

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ВолодащикТ. П.VolodashchikT.

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СкоповецЕ. Я.SkopovetsE.

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ВертелкоВ. P.VertelkoV.

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БобрикП. Ю.BobrikP.

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ШитиковаМ. Г.ShitikovaM.

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ЦехановичД. А.TsehanovichD.

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ЖеркоЛ. В.ZherkoL.

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УгловаТ. А.UglovaT.

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СолнцеваА. В.SolntsevaA.

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СаливончикА. П.SalivonchikA.

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ЗыблеваС. В.ZyblevaS.

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ХурсО. М.HursO.

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ПрибушеняО. В.PribushenyaO.

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ГУ «РНПЦ детской онкологии, гематологии и иммунологии»ГУ «РНПЦ детской онкологии, гематологии и иммунологии»ГУ «РНПЦ радиационной медицины и экологии человека»ГУ «РНПЦ радиационной медицины и экологии человека»ГУ «РНПЦ «Мать и дитя»ГУ «РНПЦ «Мать и дитя»202520102025036374Copyright © Белевцев М.В., Шарапова С.О., Гурьянова И.Е., Жаранкова Ю.С., Полякова Е.А., Алешкевич С.Н., Сакович И.С., Купчинская А.Н., Володащик Т.П., Скоповец Е.Я., Вертелко В.P., Бобрик П.Ю., Шитикова М.Г., Цеханович Д.А., Жерко Л.В., Углова Т.А., Солнцева А.В., Саливончик А.П., Зыблева С.В., Хурс О.М., Прибушеня О.В., 20252025Белевцев М.В., Шарапова С.О., Гурьянова И.Е., Жаранкова Ю.С., Полякова Е.А., Алешкевич С.Н., Сакович И.С., Купчинская А.Н., Володащик Т.П., Скоповец Е.Я., Вертелко В.P., Бобрик П.Ю., Шитикова М.Г., Цеханович Д.А., Жерко Л.В., Углова Т.А., Солнцева А.В., Саливончик А.П., Зыблева С.В., Хурс О.М., Прибушеня О.В.Belevtsev M., Sharapova S., Guryanova I., Zharankova Y., Polyakova E., Aleshkevich S., Sakovich I., Kupchinskaya A., Volodashchik T., Skopovets E., Vertelko V., Bobrik P., Shitikova M., Tsehanovich D., Zherko L., Uglova T., Solntseva A., Salivonchik A., Zybleva S., Hurs O., Pribushenya O.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://medbio.ejournal.by/jour/article/view/479

Первичные иммунодефициты (ПИД) представляют собой гетерогенную группу заболеваний, обусловленных генетически детерминированными врождёнными дефектами одного или нескольких компонентов иммунной системы. Распространённость ПИД в мире является одним из ключевых эпидемиологических показателей, позволяющих формировать оптимальную политику общественного здравоохранения в отношении их лечения и профилактики на государственном и международном уровнях. С помощью регистров удаётся показать различия этнической географической распространённости ПИД, получить данные о клинических особенностях, диагностике и вариантах лечения. С 2005 года в Республике Беларусь ведётся целенаправленная работа по оказанию медицинской помощи пациентам с ПИД. На начало 2025 года Республиканский регистр ПИД Республики Беларусь включает 774 пациента. Постоянный ежегодный рост выявления новых случаев ПИД подчёркивает прогрессивное улучшение осведомлённости врачей о первичных нарушениях иммунной системы, хотя, безусловно, необходимы дополнительные меры в данном направлении.

Primary immunodeficiencies (PIDs) are a heterogeneous group of diseases caused by genetically determined congenital defects of one or more components of the immune system. The prevalence of PIDs worldwide is one of the key epidemiological indicators that allows for the formation of optimal public health policies regarding their treatment and prevention at the national and international levels. With the help of registries, it is possible to demonstrate differences in the ethnic and geographical prevalence of PID, and to obtain data on clinical features, diagnosis, and treatment options. Since 2005, targeted work has been initiated in the Republic of Belarus to provide medical care to patients with PID. As of the beginning of 2025, the Republican PID Registry of the Republic of Belarus includes 774 patients. The constant annual increase in the detection of new cases of PID highlights the progressive improvement in physicians’ awareness of primary immune system disorders, although additional measures in this direction are clearly necessary.

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The authors declare that there are no conflicts of interest present.