medbioМедико-биологические проблемы жизнедеятельностиMedical and Biological Problems of Life Activity2074-2088Республиканский научно-практический центр радиационной медицины и экологии человекаmedbio-222Research ArticleОБМЕН ОПЫТОМEXPERIENCE EXCHANGEКлинический случай приобретенной формы тромботической тромбоцитопенической пурпуры: диагностический поиск и лечениеA clinical case of acquired form of thrombotic thrombocytopenic purpura. Description and treatmentНовикД. К.NovikD. K.noemail@neicon.ruДенисовА. В.DenisovA. V.noemail@neicon.ruРепченкоЕ. М.RepchenkoE. M.noemail@neicon.ruКравченкоД. В.KravchenkoD. V.noemail@neicon.ruКузнецовС. Г.KuzniatsouS. G.noemail@neicon.ruХадановичС. А.KhadanovichS. A.noemail@neicon.ruГУ «РНПЦ радиационной медицины и экологии человека»Russian Federation20190203202302124128Copyright © Новик Д.К., Денисов А.В., Репченко Е.М., Кравченко Д.В., Кузнецов С.Г., Хаданович С.А., 20232023Новик Д.К., Денисов А.В., Репченко Е.М., Кравченко Д.В., Кузнецов С.Г., Хаданович С.А.Novik D.K., Denisov A.V., Repchenko E.M., Kravchenko D.V., Kuzniatsou S.G., Khadanovich S.A.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://medbio.ejournal.by/jour/article/view/222

В настоящей статье изложен клинический случай приобретенной формы тромботической тромбоцитопенической пурпуры. Описаны симптоматика данного редкого заболевания и проводимое лечение. Диагноз был выставлен по минимальным диагностическим критериям и в процессе лечения был получен хороший терапевтический ответ.

In the article have described symptoms and ongoing treatment of the acquired form of thrombotic thrombocytopenic purpura.Thrombotic thrombocytopenic purpura is a rare disease with a frequency of 4:1000000 population. It is characterized by an extremely aggressive course and high mortality in the absence of treatment (up to 90%). Often has no specific symptoms. The condition for clinical diagnosis (in the absence of other causes) is the presence of at least two symptoms: thrombocytopenia, microangiopathic hemolytic anemia.

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The authors declare that there are no conflicts of interest present.